Additional pediatric resources: GeneralPediatrics.com | PediatricEducation.org | SearchingPediatrics.com
Correlapaedia - a Correlative Encyclopedia of Pediatric Imaging, Surgery, and Pathology
Clinical History:
The patient was a 4 year old male who presented to an outside institution with increased perspiration.
Clinical Physical Exam:
Unremarkable
Clinical Labs:
Non-contributory
Clinical Differential Diagnosis:
Pheochromocytoma, neuroblastoma
Imaging Findings:
A computed tomography exam of the abdomen demonstrated a large right adrenal mass.
Imaging Differential Diagnosis:
Neuroblastoma vs. pheochromocytoma
Operative Findings:
The patient was taken to the operating room at the outside institution for an exploratory laparotomy. The surgeon immobilized the right adrenal mass and found evidence of intracaval extension of tumor. The outside surgeon was unable to secure a cardiopulmonary bypass team willing to back him up for taking the tumor out of the inferior vena cava and he therefore terminated his laparotomy and sent the child to our institution for definitive surgery.
Several days later the patient underwent re-exploration by reopening his transverse right abdominal wound. A 6 cm right adrenal mass that was quite adherent to the inferior vena cava was found. There was tumor extension of about the size of a marble into the cava through the adrenal vein. A right adrenalectomy with removal of the intracaval extension of tumor was performed.
Pathological Findings:
Examination of the surgical specimen revealed characteristic findings of pheochromocytoma.
Final Diagnosis:
Pheochromocytoma (Right Adrenal)
Follow-up and Prognosis:
The patient had a history of familial pheochromocytoma, with his father and sister having undergone bilateral adrenalectomies for pheochromocytoma. The patient had an uncomplicated post-operative course.
Similar Cases:
None
References:
Additional pediatric resources: GeneralPediatrics.com | PediatricEducation.org | SearchingPediatrics.com
Please send us comments by filling out our Comment Form.
All contents copyright © 1992-2023 Donna M. D'Alessandro, M.D. and Michael P. D'Alessandro, M.D. and the authors. All rights reserved.
"Virtual Pediatric Hospital", the Virtual Pediatric Hospital logo, and "A digital library of pediatric information" are all Trademarks of Donna M. D'Alessandro, M.D. and Michael P. D'Alessandro, M.D.
Virtual Pediatric Hospital is funded in whole by Donna M. D'Alessandro, M.D. and Michael P. D'Alessandro, M.D. Advertising is not accepted.
Your personal information remains confidential and is not sold, leased, or given to any third party be they reliable or not.
The information contained in Virtual Pediatric Hospital is not a substitute for the medical care and advice of your physician. There may be variations in treatment that your physician may recommend based on individual facts and circumstances.
URL: http://www.virtualpediatrichospital.org/
Images 1, 2, and 3
Image 4
Image 5
Image 6
Image 7