Correlapaedia - a Correlative Encyclopedia of Pediatric Imaging, Surgery, and Pathology

Case 52

Clinical History:
The patient was a female born electively at 38 weeks gestation with a large anterior abdominal wall defect that was diagnosed by prenatal ultrasound at 20 weeks. She also had a ventricular septal defect via echocardiography.

Images 1 and 2

Clinical Physical Exam:
Large omphalocele

Clinical Labs:
Non-contributory

Clinical Differential Diagnosis:
Omphalocele

Imaging Findings:
A chest film from the first day of life showed a large omphalocele.

Image 3

Imaging Differential Diagnosis:
Omphalocele

Operative Findings:
On the second day of life the patient underwent repair of the omphalocele defect. It could not be closed primarily. A Silon mesh silo was placed and progressively tightened over several days. A final closure of the anterior abdominal wall defect was performed on the eleventh day of life.

Pathological Findings:
None

Final Diagnosis:
Omphalocele

Follow-up and Prognosis:
The patient developed pyloric stenosis post operatively which was treated surgically on the fortieth day of life.

Similar Cases:
Case 3, Case 19, Case 25

References:

• Paediapedia
• WebPath
• WebPath
• WebPath

Title Page

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