Virtual Pediatric Hospital(tm) : A digital library of pediatric information

Home | About Us | FAQ | Reviews | Search

Additional pediatric resources: GeneralPediatrics.com | PediatricEducation.org | SearchingPediatrics.com


Virtual Pediatric Hospital: Paediapaedia: Familial Polyposis Paediapaedia: Gastrointestinal Diseases

Familial Polyposis

Michael P. D'Alessandro, M.D.
Peer Review Status: Internally Peer Reviewed


Clinical Presentation:
Presents by approximately 10 years of age with painless rectal bleeding.

Etiology/Pathophysiology:
Tranmission as autosomal dominant, but 50% of cases arise spontaneously. The lesions start off being sessile and become pedunculated over time. The polyps are adenomatous with malignant potential and need treatment via a total colectomy as 95% of patients who do not have a colectomy develop colon carcinoma by the 5th decade. The most frequently involved site is the sigmoid.

Pathology:
Not applicable

Imaging Findings:
On an air contrast enema in older patients multiple polyps of relatively uniform size and configuration are seen, ranging from 2-4 millimeters in diameter, that coat the colonic mucosa. In younger patients you may only see serrations of the colonic mucosa that resembles ulcerative colitis.

DDX:

References:
See References Chapter.

Section Top | Title Page


Home | About Us | FAQ | Reviews | Search

Additional pediatric resources: GeneralPediatrics.com | PediatricEducation.org | SearchingPediatrics.com


Virtual Pediatric Hospital is curated by Donna M. D'Alessandro, M.D. and by Michael P. D'Alessandro, M.D.

Please send us comments by filling out our Comment Form.

All contents copyright © 1992-2024 Donna M. D'Alessandro, M.D. and Michael P. D'Alessandro, M.D. and the authors. All rights reserved.

"Virtual Pediatric Hospital", the Virtual Pediatric Hospital logo, and "A digital library of pediatric information" are all Trademarks of Donna M. D'Alessandro, M.D. and Michael P. D'Alessandro, M.D.

Virtual Pediatric Hospital is funded in whole by Donna M. D'Alessandro, M.D. and Michael P. D'Alessandro, M.D. Advertising is not accepted.

Your personal information remains confidential and is not sold, leased, or given to any third party be they reliable or not.

The information contained in Virtual Pediatric Hospital is not a substitute for the medical care and advice of your physician. There may be variations in treatment that your physician may recommend based on individual facts and circumstances.

URL: http://www.virtualpediatrichospital.org/