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Virtual Pediatric Hospital: Thoracopaedia: An Imaging Encyclopedia of Pediatric Thoracic Disease: Case 31 Thoracopaedia: An Imaging Encyclopedia of Pediatric Thoracic Disease

Case 31

Michael P. D'Alessandro, M.D.
Peer Review Status: Internally Peer Reviewed


Chief Complaint:
Eleven year old male being evaluated for lung transplantation

Clinical History:
The patient was an 11 year old male with severe cystic fibrosis being evaluated for lung transplantation.

Clinical Physical Exam:
Respiratory distress.

Clinical Labs:
Non-contributory

Clinical Differential Diagnosis:
Cystic fibrosis

Imaging Findings:
Chest films showed a coarse interstitial pattern, bronchial wall thickening, and bronchiectasis. Chest CT exam confirmed and better displayed the findings.

icon gificon gifImages 1 and 2

icon gificon gifImages 3, 4, and 5

Imaging Differential Diagnosis:
Cystic fibrosis

Operative Findings:
None

Pathological Findings:
None

Final Diagnosis:
Cystic Fibrosis

Follow-up and Prognosis:
Not available.

Similar Cases:
None

References:

Title Page


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